UniProt/SwissProt ID: | CFTR_HUMAN |
Description: | cystic fibrosis transmembrane conductance regulator (ATP-binding cassette sub-family C, member 7) [Source:HGNC Symbol;Acc:1884] |
Location: | chr7 q31.2 |
Node attribute: | substrate; gene |
Phosphorylation site |
Position | PhosphoPeptide | Catalytic kinase | Source |
---|---|---|---|
S660 | AERRNsILTET | CFTR_R | PhosphoSitePlus |
S700 | EKRKNsILNPI | PRKG1 | HPRD |
S1362 | ARSVLsKAKIL | HPRD | |
S712 | SIRKFsIVQKT | phosphoELM; RegPhos | |
S686 | ETKKQsFKQTG | PKCa(PKC alpha | RegPhos |
S813 | YSRRLsQETGL | PKG_group | RegPhos |
S686 | ETKKQsFKQTG | CFTR_R | PhosphoSitePlus |
S768 | ARRRQsVLNLM | PKACa | RegPhos |
S795 | STRKVsLAPQA | PRKACA | HPRD |
S737 | LERRLsLVPDS | PRKACA | HPRD |
S795 | STRKVsLAPQA | PKACa | RegPhos |
T1019 | YIFVAtVPVIV | TM; ABC_membrane | PhosphoSitePlus |
Y515 | VSYDEyRYRSV | ABC_tran | PhosphoSitePlus |
S422 | NNRKTsNGDDS | Rotamase_2 | PhosphoSitePlus |
S768 | ARRRQsVLNLM | PKG/cGK_group | phosphoELM |
S768 | ARRRQsVLNLM | PRKG1 | HPRD |
S795 | STRKVsLAPQA | PKG/cGK_group | phosphoELM |
T291 | ENLRQtELKLT | HPRD | |
S753 | ILPRIsVISTG | PKA_group | phosphoELM; RegPhos |
S790 | RKTTAsTRKVS | PRKCA | HPRD |
S768 | ARRRQsVLNLM | PKG_group | RegPhos |
S768 | ARRRQsVLNLM | PKA_group | phosphoELM; RegPhos |
S737 | LERRLsLVPDS | PKG_group | RegPhos |
S686 | ETKKQsFKQTG | PRKCA | HPRD |
S795 | STRKVsLAPQA | PKG_group | RegPhos |
S660 | AERRNsILTET | PKG1 | RegPhos |
S660 | AERRNsILTET | PRKG1 | HPRD |
S686 | ETKKQsFKQTG | PKCa | RegPhos |
S700 | EKRKNsILNPI | PKG_group | RegPhos |
S795 | STRKVsLAPQA | CFTR_R | PhosphoSitePlus |
S813 | YSRRLsQETGL | PKA_group | phosphoELM; RegPhos |
Y1014 | AVLQPyIFVAT | TM; ABC_membrane | PhosphoSitePlus |
T682 | VSWTEtKKQSF | CFTR_R | PhosphoSitePlus |
S700 | EKRKNsILNPI | PKG/cGK_group | phosphoELM |
S641 | LQPDFsSKLMG | CFTR_R | PhosphoSitePlus |
S707 | LNPINsIRKFS | CFTR_R | PhosphoSitePlus |
S686 | ETKKQsFKQTG | PKC_alpha | phosphoELM |
S813 | YSRRLsQETGL | PKG/cGK_group | phosphoELM |
S790 | RKTTAsTRKVS | CFTR_R | PhosphoSitePlus |
Y512 | IFGVSyDEYRY | ABC_tran | PhosphoSitePlus |
T291 | ENLRQtELKLT | ABC_membrane | PhosphoSitePlus |
S737 | LERRLsLVPDS | PRKG1 | HPRD |
S813 | YSRRLsQETGL | PKG1 | RegPhos |
T582 | YLDVLtEKEIF | PhosphoSitePlus | |
S700 | EKRKNsILNPI | PKG1 | RegPhos |
T604 | TRILVtSKMEH | PhosphoSitePlus | |
S712 | SIRKFsIVQKT | CFTR_R | PhosphoSitePlus |
S768 | ARRRQsVLNLM | CFTR_R | PhosphoSitePlus |
S813 | YSRRLsQETGL | CFTR_R | PhosphoSitePlus |
S605 | RILVTsKMEHL | PhosphoSitePlus | |
T1176 | TEGKPtKSTKP | HPRD | |
S790 | RKTTAsTRKVS | PKC_group | phosphoELM; RegPhos |
S700 | EKRKNsILNPI | CFTR_R | PhosphoSitePlus |
S712 | SIRKFsIVQKT | PKA_group | RegPhos |
S776 | NLMTHsVNQGQ | CFTR_R | PhosphoSitePlus |
S813 | YSRRLsQETGL | PKACa | RegPhos |
S660 | AERRNsILTET | PKG/cGK_group | phosphoELM |
S768 | ARRRQsVLNLM | PKG1 | RegPhos |
S737 | LERRLsLVPDS | PKG/cGK_group | phosphoELM |
S700 | EKRKNsILNPI | PRKACA | HPRD |
S686 | ETKKQsFKQTG | PKC_group | phosphoELM; RegPhos |
S700 | EKRKNsILNPI | PKACa | RegPhos |
S549 | GGITLsGGQRA | HPRD | |
S549 | GGITLsGGQRA | ABC_tran | PhosphoSitePlus |
S813 | YSRRLsQETGL | PRKACA | HPRD |
S737 | LERRLsLVPDS | CFTR_R | PhosphoSitePlus |
S753 | ILPRIsVISTG | CFTR_R | PhosphoSitePlus |
S700 | EKRKNsILNPI | PKA_group | phosphoELM; RegPhos |
S1362 | ARSVLsKAKIL | ABC_tran | PhosphoSitePlus |
S768 | ARRRQsVLNLM | PRKACA | HPRD |
S660 | AERRNsILTET | PKG_group | RegPhos |
S813 | YSRRLsQETGL | PRKG1 | HPRD |
S737 | LERRLsLVPDS | PKACa | RegPhos |
S511 | IIFGVsYDEYR | ABC_tran | PhosphoSitePlus |
S795 | STRKVsLAPQA | PKA_group | phosphoELM; RegPhos |
S256 | RAGKIsERLVI | ABC_membrane | PhosphoSitePlus |
T774 | VLNLMtHSVNQ | CFTR_R | PhosphoSitePlus |
S795 | STRKVsLAPQA | PKG1 | RegPhos |
S795 | STRKVsLAPQA | PRKG1 | HPRD |
Y1424 | NKVRQyDSIQK | PhosphoSitePlus | |
S809 | ELDIYsRRLSQ | CFTR_R | PhosphoSitePlus |
S737 | LERRLsLVPDS | PKG1 | RegPhos |
S737 | LERRLsLVPDS | PKA_group | phosphoELM; RegPhos |
S790 | RKTTAsTRKVS | PKCa | RegPhos |
T1471 | ALKEEtEEEVQ | PhosphoSitePlus | |
S660 | AERRNsILTET | PKA_group | phosphoELM; RegPhos |
Dephosphorylation site |
CFTR_HUMAN do not have dephosphorylation site. |
Mutation site |
Ensembl ID | Variation | Source | Cancer name | Pubmed |
---|---|---|---|---|
ENSP00000003084 | Q1071* | BIOMART | Pancreatic Cancer | 21930507, 21930502 |
ENSP00000003084 | S1248L | COSMIC | Melanoma | 21499247 |
ENSP00000003084 | P355S | COSMIC | Melanoma | 21499247 |
ENSP00000403677 | F855I | BIOMART | Breast Cancer | 21930507, 21930502 |
ENSP00000003084 | F916I | BIOMART | Breast Cancer | 21930507, 21930502 |
ENSP00000003084 | S108Y | TCGA | Ovarian Cancer | 21720365, 18772890 |
ENSP00000003084 | Q414K | BIOMART | Breast Cancer | 21930507, 21930502 |
ENSP00000003084 | P205S | COSMIC | Skin Cancer | 21984974 |
ENSP00000003084 | N386K | COSMIC | Ovarian Cancer | 21720365 |
ENSP00000403677 | Q1010* | BIOMART | Pancreatic Cancer | 21930507, 21930502 |
ENSP00000003084 | E608K | COSMIC | Skin Cancer | 21984974 |
ENSP00000003084 | S108Y | COSMIC | Ovarian Cancer | 21720365 |
Differential expressed protein |
CFTR_HUMAN is not differential expressed protein. |
Hyperphosphorylation site |
CFTR_HUMAN do not have hyperphosphorylation site. |
Direct Interaction Pair |
Source | Target | Relationship | Resource |
---|---|---|---|
KPCA_HUMAN | CFTR_HUMAN | kinase -> substrate | HPRD; Robert H Newman (2013) |
ZAGL2_HUMAN | CFTR_HUMAN | kinase -> substrate | RegPhos |
KGP1_HUMAN | CFTR_HUMAN | kinase -> substrate | HPRD |
CEBPD_HUMAN | CFTR_HUMAN | TF -> target gene | TRANSFAC |
CREB1_HUMAN | CFTR_HUMAN | TF -> target gene | TRANSFAC |
Function Annotation |
KEGG Pathway |
KEGG ID | Pathway |
---|---|
hsa04971 | Gastric acid secretion |
hsa05110 | Vibrio cholerae infection |
hsa02010 | ABC transporters |
hsa04972 | Pancreatic secretion |
hsa04976 | Bile secretion |
Gene Ontology |
GO ID | GO_Term | Evidence | Ontology |
---|---|---|---|
GO:0000166 | nucleotide binding | IEA | molecular_function |
GO:0005886 | plasma membrane | IDA | cellular_component |
GO:0042626 | ATPase activity, coupled to transmembrane movement | IEA | molecular_function |
GO:0032870 | cellular response to hormone stimulus | IEA | biological_process |
GO:0005254 | chloride channel activity | IDA | molecular_function |
GO:0043434 | response to peptide hormone stimulus | IEA | biological_process |
GO:0005524 | ATP binding | IEA | molecular_function |
GO:0006810 | transport | TAS | biological_process |
GO:0019869 | chloride channel inhibitor activity | IDA | molecular_function |
GO:0016887 | ATPase activity | IEA | molecular_function |
GO:0016020 | membrane | IEA | cellular_component |
GO:0030321 | transepithelial chloride transport | IEA | biological_process |
GO:0016324 | apical plasma membrane | IEA | cellular_component |
GO:0043627 | response to estrogen stimulus | IEA | biological_process |
GO:0005515 | protein binding | IPI | molecular_function |
GO:0015705 | iodide transport | IEA | biological_process |
GO:0055085 | transmembrane transport | TAS | biological_process |
GO:0006821 | chloride transport | IEA | biological_process |
GO:0005260 | channel-conductance-controlling ATPase activity | NAS | molecular_function |
GO:0005769 | early endosome | IDA | cellular_component |
GO:0031901 | early endosome membrane | IEA | cellular_component |
GO:0043234 | protein complex | IDA | cellular_component |
GO:0042311 | vasodilation | IEA | biological_process |
GO:0006811 | ion transport | IEA | biological_process |
GO:0031205 | endoplasmic reticulum Sec complex | IDA | cellular_component |
GO:0034097 | response to cytokine stimulus | IEA | biological_process |
GO:0015701 | bicarbonate transport | IEA | biological_process |
GO:0042493 | response to drug | IEA | biological_process |
GO:0030301 | cholesterol transport | IEA | biological_process |
GO:0016021 | integral to membrane | IEA | cellular_component |
GO:0045909 | positive regulation of vasodilation | IEA | biological_process |
GO:0005224 | ATP-binding and phosphorylation-dependent chloride | TAS | molecular_function |
GO:0034707 | chloride channel complex | IEA | cellular_component |
GO:0005902 | microvillus | IEA | cellular_component |
GO:0007585 | respiratory gaseous exchange | TAS | biological_process |
GO:0030165 | PDZ domain binding | IDA | molecular_function |
GO:0017111 | nucleoside-triphosphatase activity | IEA | molecular_function |
GO:0030324 | lung development | IEA | biological_process |
GO:0006695 | cholesterol biosynthetic process | IEA | biological_process |
GO:0030659 | cytoplasmic vesicle membrane | IEA | cellular_component |
GO:0019899 | enzyme binding | IPI | molecular_function |
GO:0016323 | basolateral plasma membrane | IEA | cellular_component |
GO:0006833 | water transport | IEA | biological_process |
GO:0005737 | cytoplasm | IEA | cellular_component |